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P121Pulmonary valve atresia. Fetal echocardiography findings in one case with intact ventricular septum
Author(s) -
García C.,
Lagos N.,
Diaz C.,
Meneses N.,
Castillo G.,
Pazols R.,
Benavides C.,
Hoffmann I.,
Ortega P.,
Ferres I.
Publication year - 2000
Publication title -
ultrasound in obstetrics and gynecology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 3.202
H-Index - 141
eISSN - 1469-0705
pISSN - 0960-7692
DOI - 10.1046/j.1469-0705.2000.00004-1-120.x
Subject(s) - medicine , pulmonary atresia , cardiology , interventricular septum , regurgitation (circulation) , heart failure , pulmonary valve , fetal echocardiography , coarctation of the aorta , heart disease , tricuspid valve , prenatal diagnosis , fetus , aorta , pregnancy , ventricle , biology , genetics
Background Right ventricular outflow obstruction with an intact ventricular septum leads to severe hemodynamic problems in the newborn, with hypoxemia and congestive heart failure due to tricusp regurgitation. Atresia of the pulmonary valve occurs in less than 3% of all congenital heart lesions, with a frequency of 1:25 000 of live births. Use of fetal echocardiography permits prenatal diagnosis of this and other congenital defects, for a better knowledge and therapy. Case report 35‐year‐old pacient, with a previous newborn with an interventricular comunication. On her 30 week of pregnancy, a fetal echocardiography showed atresia of the pulmonary valve with an intact interventricular septum, severe tricuspid regurgitation, a right atrial dilatation, restriction of flow in the oval foramen of 8 m/seg and ductus arterioso with retrograde or bidirectional flow, from the aorta to the pulmonary circulation. Vaginal delivery occurred at 38 weeks, obtaining a female newborn, 2630 g, in good conditions. However she developed severe cardiac failure and died at day 4, in spite of pharmacologic with prostaglandins and surgical therapy. Conclusions Echocardiography is the basis of prenatal diagnosis of congenital heart disease, like pulmonary valve atresia, and is of great help to understand and decide the best perinatal therapy.