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Antenatal sonographic findings associated with scimitar syndrome
Author(s) -
Grisaru D.,
Achiron R.,
Lipitz S.,
Yahav J.,
Hegesh J.,
Rotstein Z.
Publication year - 1996
Publication title -
ultrasound in obstetrics and gynecology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 3.202
H-Index - 141
eISSN - 1469-0705
pISSN - 0960-7692
DOI - 10.1046/j.1469-0705.1996.08020131.x
Subject(s) - scimitar syndrome , medicine , right pulmonary artery , inferior vena cava , lung , pulmonary hypoplasia , diaphragm (acoustics) , cardiology , pulmonary artery , pulmonary sequestration , fetus , radiology , fetal echocardiography , descending aorta , hypoplasia , aorta , prenatal diagnosis , pregnancy , genetics , physics , biology , acoustics , loudspeaker
Scimitar syndrome is a rare congenital anomaly that consists of secondary dextroposition in situs solitus, due to right pulmonary hypoplasia. The prenatal sonographic findings of this abnormality have not been previously described. We describe early sonographic findings in a fetus that included isolated cardiac dextroposition with normal abdominal situs, hydramnios and mild narrowing of the right pulmonary artery. Postnatally, the infant developed heart failure, and a right hypoplastic lung was found. Catheterization revealed collateral supply to the right lung arising from the descending aorta and anomalous drainage of right pulmonary veins to the inferior vena cava. The diagnosis of scimitar syndrome was therefore established. A coil embolization of arterial collaterals to the right lung was performed. Scimitar syndrome should be considered in a fetus with the sonographic findings of a right shift of the mediastinal structures, an intact diaphragm and narrow right pulmonary artery. This may allow early neonatal stabilization and treatment. Copyright © 1996 International Society of Ultrasound in Obstetrics and Gynecology