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Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia: A Case Report of Identical Twins with Heart Failure
Author(s) -
INDIK JULIA H.,
SMITH DAVID E.,
SOBONYA RICHARD E.,
MARCUS FRANK I.
Publication year - 2002
Publication title -
pacing and clinical electrophysiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.686
H-Index - 101
eISSN - 1540-8159
pISSN - 0147-8389
DOI - 10.1046/j.1460-9592.2002.01387.x
Subject(s) - medicine , arrhythmogenic right ventricular dysplasia , cardiology , heart failure , cardiomyopathy , dysplasia , sudden death , sudden cardiac death , heart disease
INDIK, J.H., et al. : Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia: A Case Report of Identical Twins with Heart Failure. Arrhythmogenic right ventricular cardiomyopathy/dysplasia is characterized by the progressive replacement of myocardium by fatty or fibrofatty tissue. Presenting symptoms are generally related to ventricular arrhythmias, including sudden cardiac death. Heart failure due to right ventricular and sometimes left ventricular dysfunction is uncommon in the early stages of the disease, but is known to occur in advanced cases. This case report describes identical adolescent twins with presenting symptoms related predominantly to right heart failure.