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Anaesthetic management of a prematurely born infant with Cantrell's Pentalogy
Author(s) -
LALOYAUX PIERRE,
VEYCKEMANS FRANCIS,
VAN DYCK MICHEL
Publication year - 1998
Publication title -
pediatric anesthesia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.704
H-Index - 82
eISSN - 1460-9592
pISSN - 1155-5645
DOI - 10.1046/j.1460-9592.1998.00687.x
Subject(s) - medicine , surgery , diaphragmatic breathing , omphalocele , diaphragmatic hernia , pericardium , sternum , abdominal wall , hernia , pregnancy , fetus , alternative medicine , pathology , biology , genetics
Cantrell's pentalogy (CP) is a rare congenital syndrome combining a defect of the supraumbilical abdominal wall, the agenesis of the lower part of the sternum and of the anterior portion of the diaphragm, the absence of the diaphragmatic part of the pericardium, and a cardiac malformation. It was first described by Cantrell in 1958 (1,2). We report the case of a prematurely born infant with CP and Wolff–Parkinson–White (WPW) syndrome who required surgery first for bilateral inguinal hernia repair and later for Blalock–Taussig shunt. During these two procedures, our anaesthetic plan was to preserve the fragile equilibrium of both the pulmonary and the cardiovascular systems.