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Use of a retrograde femoral nail in a patient with M c Cune−Albright syndrome
Author(s) -
Garvan John D.,
Trantalis John N.
Publication year - 2003
Publication title -
anz journal of surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.426
H-Index - 70
eISSN - 1445-2197
pISSN - 1445-1433
DOI - 10.1046/j.1445-2197.2003.t01-4-.x
Subject(s) - medicine , polyostotic fibrous dysplasia , fibrous dysplasia , mccune–albright syndrome , surgery , deformity , perioperative , internal fixation , bone grafting , femur , precocious puberty , hormone
McCune−Albright Syndrome is a rare condition characterized by endocrine abnormalities, precocious puberty, pigmented skin lesions and polyostotic fibrous dysplasia with consequent fractures and limb deformity. Patients with this syndrome might have had multiple operations on a limb and might also have extensive internal fixation in‐situ . We review the case of a 41‐year‐old woman with McCune−Albright syndrome, who presented with a pathological fracture of her left femur below a long plate and screws. Our management of this challenging problem included the use of a retrograde femoral nail, which, because of the need to retain pre‐existing internal fixation, had to be locked proximally through a hole in a femoral plate. This technique, combined with reaming, and thus bone grafting of the fracture, and also perioperative infusions of pamidronate, allowed an early recovery and return to premorbid function for the patient. In the present study we detail our technique and discuss its advantages over other possible methods of treatment.