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Orbital lipomatous haemangiopericytoma: an unusual variant
Author(s) -
Davies Peter EJ,
Davis Garry J,
Dodd Tom,
Selva Dinesh
Publication year - 2002
Publication title -
clinical and experimental ophthalmology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.3
H-Index - 74
eISSN - 1442-9071
pISSN - 1442-6404
DOI - 10.1046/j.1442-9071.2002.00542.x
Subject(s) - medicine , orbit (dynamics) , hemangiopericytoma , radiology , pathology , engineering , aerospace engineering
Haemangiopericytoma (HPC) of the orbit is a rare tumour occurring in all age groups and presenting with slowly progressive proptosis, ocular motility impairment and visual loss. Although most are benign tumours that are resectable at diagnosis, one‐third of these tumours demonstrate malignant features and recur locally or metastasize, usually with a fatal outcome. In 1995, a morphologically unique variant, termed lipomatous haemangiopericytoma (L‐HPC), was described. Only one case has been reported previously arising in the orbit. In this paper, a case is reported of L‐HPC occurring in the orbit and consider the prognostic implications of this HPC variant.