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Peripheral primitive neuroectodermal tumor of the small bowel mesentery: A case showing perforation at onset
Author(s) -
Horie Yasushi,
Kato Masako
Publication year - 2000
Publication title -
pathology international
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.73
H-Index - 74
eISSN - 1440-1827
pISSN - 1320-5463
DOI - 10.1046/j.1440-1827.2000.01045.x
Subject(s) - mesentery , pathology , cd99 , medicine , synaptophysin , perforation , anatomy , vimentin , diaphragm (acoustics) , immunohistochemistry , materials science , physics , acoustics , loudspeaker , punching , metallurgy
A case of peripheral primitive neuroectodermal tumor of the small bowel mesentery with an uncommon clinical onset is reported. A 40‐year‐old man was admitted to hospital because of acute severe abdominal pain. Chest X‐ray revealed a free air sign beneath the diaphragm. At emergency surgery a mass measuring 11.0 × 8.0 cm with perforation was located in the jejunal mesenteric region. Histologically the resected lesion consisted of sheets of undifferentiated small round cells forming abortive Homer Wright rosettes. Some spindle‐shaped cells showed perivascular pseudorosettes. Immunohistochemical study revealed that the tumor cells expressed positivity against CD99 (MIC2), neuron‐specific enolase, synaptophysin and vimentin. To the authors’ knowledge this is the first documentation of peripheral primitive neuroectodermal tumor of the small bowel mesentery with perforation at onset.