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The dentofacial manifestations of XXXXY syndrome: a case report
Author(s) -
Hata S.,
Maruyama Y.,
Fujita Y.,
Mayanagi H.
Publication year - 2001
Publication title -
international journal of paediatric dentistry
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.183
H-Index - 62
eISSN - 1365-263X
pISSN - 0960-7439
DOI - 10.1046/j.1365-263x.2001.00253.x
Subject(s) - medicine , maxilla , orthodontics , mandible (arthropod mouthpart) , molar , dentistry , botany , biology , genus
This paper presents a six‐year‐old patient with XXXXY syndrome, whose oral findings included a cleft soft palate, hyper‐ or meso‐taurodontism in eight primary molars and in the mandibular permanent first molars, five congenitally missing premolars, and delayed development of the permanent tooth germs. The maxillary and mandibular primary central incisors were in a cross‐bite relationship. Cephalometric findings showed a short ramus of the mandible and a short maxilla in the anterio‐posterior plane. The anteroposterior jaw relationship was in harmony. The cross‐bite was considered to be due to the retroinclination of the maxillary primary incisors. This case emphasises the importance of regular dental care, and monitoring of facial growth and dental development in children with XXXXY syndrome.