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Surgery in severe factor XIII deficiency: report of a case of epilepsy neurosurgery and review
Author(s) -
Pernod G.,
Barro C.,
Arnutti B.,
BlancJouvan F.,
Garrel S.,
Kahn P.,
Minotti L.,
Koudsie A.,
Benabid A. L.,
Wrobleski I.,
Joannard A.,
Polack B.
Publication year - 2003
Publication title -
haemophilia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.213
H-Index - 92
eISSN - 1365-2516
pISSN - 1351-8216
DOI - 10.1046/j.1365-2516.2003.00700.x
Subject(s) - medicine , neurosurgery , epilepsy , epilepsy surgery , seizure disorders , surgery , factor xiii deficiency , pediatrics , intractable epilepsy , factor xiii , psychiatry , fibrinogen
Summary. Factor XIII (FXIII) deficiency is a rare autosomal recessive congenital disorder of haemostasis, associated with a high risk of intracranial haemorrhage. Intracranial haemorrhage can result in neurological sequelae including seizure disorders. In some cases, medically intractable epilepsy led to epilepsy surgery. Little has been reported on the management of FXIII deficiency during surgery, and there is only a few data on the management, safety and efficacy of epilepsy surgery in the patients with haemostatic disorder. We report here an epilepsy neurosurgery in a case of severe FXIII deficiency.