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von Willebrand disease in Finland
Author(s) -
Kekomäki R.,
Rasi V.,
Ebeling F.,
Vahtera E.,
Javela K.,
Koski T.,
Myllylä G.,
Ikkala E.
Publication year - 1999
Publication title -
haemophilia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.213
H-Index - 92
eISSN - 1365-2516
pISSN - 1351-8216
DOI - 10.1046/j.1365-2516.1999.0050s2072.x
Subject(s) - medicine , von willebrand disease , von willebrand factor , pediatrics , disease , coagulation , platelet
The Finnish Red Cross Blood Transfusion Service has served as the national reference laboratory for haemostasis for more than 40 years and remains still the only one in the country to diagnose inherited coagulation factor deficiencies. By September 1997, 1076 patients with von Willebrand disease (vWD) were registered. The severity of bleeding symptoms leading to diagnosis varied according to the type of vWD. After prepubertal phase distinctly more female than male patients were diagnosed. The prevalence of severe type 3 vWD is 4:1 000 000.