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Primary lymphoedema associated with xanthomatosis, vaginal lymphorrhoea and intestinal lymphangiectasia
Author(s) -
Karg E.,
Bereczki C.,
Kovacs J.,
Korom I.,
Varkonyi A.,
Megyeri P.,
Turi S.
Publication year - 2002
Publication title -
british journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 2.304
H-Index - 179
eISSN - 1365-2133
pISSN - 0007-0963
DOI - 10.1046/j.1365-2133.2002.04477.x
Subject(s) - lymphangiectasia , medicine , lymphedema , reflux , biopsy , girl , dermatology , lymphatic system , pathology , disease , cancer , psychology , developmental psychology , breast cancer
Primary lymphoedema associated with chylous reflux is a very rare clinical entity. We report a 3‐year‐old girl with unilateral lymphoedema, xanthomatosis and vaginal lymphorrhoea. Biopsy also revealed intestinal lymphangiectasia. This paper also presents a brief review of the literature and draws attention to the significance of the xanthomatous eruption in the diagnosis of a chylous reflux.