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Hereditary benign telangiectasia: image analysis of hitherto unknown association with arteriovenous malformation
Author(s) -
Onishi Y.,
Ohara K.,
Shikada Y.,
Satomi H.
Publication year - 2001
Publication title -
british journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 2.304
H-Index - 179
eISSN - 1365-2133
pISSN - 0007-0963
DOI - 10.1046/j.1365-2133.2001.04446.x
Subject(s) - telangiectasia , medicine , arteriovenous malformation , radiology , angiography , pathology
We report 10 patients with hereditary benign telangiectasia (HBT), in whom the age ranged from 1 to 19 years (mean 7·5). The male/female ratio was 1 : 2·3 (3 : 7). Four patients (40%) had congenital lesions. Image analysis with Doppler echogram, angiography and thermography revealed an arterial component in the lesions, consistent with arteriovenous malformation (AVM). This is the first report of HBT in association with AVM.