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Unstable angina associated with coronary arterial calcification in a thalassemia intermedia patient with a pseudoxanthoma elasticum‐like syndrome
Author(s) -
Farmakis Dimitrios,
Moyssakis Ioannis,
Perakis Alexandros,
Rombos Yiannis,
Deftereos Spyros,
Giakoumis Anastasios,
Polymeropoulos Evangelos,
Aessopos Athanasios
Publication year - 2003
Publication title -
european journal of haematology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.904
H-Index - 84
eISSN - 1600-0609
pISSN - 0902-4441
DOI - 10.1034/j.1600-0609.2003.02846_70_1.x
Subject(s) - pseudoxanthoma elasticum , medicine , cardiology , calcification , thalassemia , angina , unstable angina , calcinosis , hemolytic anemia , pathology , coronary heart disease , myocardial infarction
Abstract: The coexistence of a pseudoxanthoma elasticum (PXE)‐like syndrome in β‐thalassemia and other hemoglobinopathies is a recently established clinical entity that has been observed with a significant frequency and related to some severe, even life‐threatening complications. We present here a thalassemia intermedia patient who developed unstable angina in a setting of severe anemia and PXE‐related coronary arterial calcification. Besides the clinical significance of this PXE‐like syndrome, its acquired nature may introduce some new thoughts regarding the pathogenesis of atherosclerosis.