Open AccessOcular manifestations of incontinentia pigmenti
Author(s) -
Holmström G.,
Thorén K.
Publication year - 2000
Publication title -
acta ophthalmologica scandinavica
Language(s) - English
Resource type - Journals
eISSN - 1600-0420
pISSN - 1395-3907
DOI - 10.1034/j.1600-0420.2000.078003348.x
Subject(s) - medicine , incontinentia pigmenti , ophthalmology , visual acuity , blindness , retinal , dermatology , optometry , pediatrics
. Purpose: The study aimed to evaluate the ocular manifestations in patients with incontinentia pigmenti (IP). Methods: Thirty patients from different parts of Sweden participated. Orthoptic and ocular examinations were performed as well as evaluation of refraction and visual acuity. Results: Ocular manifestations, probably associated with IP, were found in 77% (23/30) of the patients. Thirteen had serious or vision‐threatening eye manifestations in one eye, of whom 7 were totally blind in that eye from retinal detachments. Ten patients had minor retinal and/or corneal changes. Conclusion: Ocular lesions in patients with IP may be serious and lead to blindness because of retinal disease. Ophthalmological follow‐up is essential in the neonatal period and such a programme is recommended.