Open Access
Sarcoidosis in childhood. A rare systemic disease
Author(s) -
Antonio Zamora-Chávez,
Stanislaw Sadowinski-Pine,
Carlos Alberto Serrano-Bello,
Luis Velázquez-Jones,
Omar Josué Saucedo-Ramírez,
Jonathan Palafox-Flores,
Erandi Josefina Mata-Vázquez
Publication year - 2016
Publication title -
boletín médico del hospital infantil de méxico
Language(s) - English
Resource type - Journals
ISSN - 2444-3409
DOI - 10.1016/s2444-3409(16)30008-5
Subject(s) - sarcoidosis , medicine , erythema nodosum , dermatology , etiology , systemic disease , disease , pathology
AbstractBackgroundSarcoidosis is a systemic disease of unknown etiology that rarely occurs in children. It usually affects the lungs; however, it may involve various organs. It occasionally affects the general condition, and causes fever, hepatomegaly and splenomegaly.Case reportWe report the case of a twelve-year-old adolescent with late-onset childhood sarcoidosis which diagnosis was confirmed by lymph node histopathological study. The patient presented general condition, hypercalcemia, erythema nodosum, severe lung disorders, lymphadenopathy, hepatomegaly and testicular mass. He received treatment with steroids, with excellent clinical response.ConclusionsWe highlight the importance of considering the diagnosis of sarcoidosis in patients with hepatomegaly, lymphadenopathy, diffuse lung damage, erythema nodosum, testicular mass and hypercalcemia, as well as the need for a multidisciplinary approach to assess multiple organ involvement and the early beginning of steroid treatment in order to prevent the progression of the disease