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A case of central odontogenic fibroma of the mandible in a nevoid basal cell carcinoma syndrome patient
Author(s) -
Shimada Yasuyuki,
Kawasaki Yohei,
Tayama Michita,
Kindaichi Junko,
Maruoka Yutaka
Publication year - 2018
Publication title -
oral science international
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.256
H-Index - 13
eISSN - 1881-4204
pISSN - 1348-8643
DOI - 10.1016/s1348-8643(17)30056-3
Subject(s) - keratocyst , nevoid basal cell carcinoma syndrome , mandible (arthropod mouthpart) , odontogenic , medicine , basal cell nevus syndrome , maxilla , basal cell , dermatology , basal cell carcinoma , pathology , dentistry , biology , botany , genus
Nevoid basal cell carcinoma syndrome (NBCCS) is an autosomal dominant disorder characterized by tumorigenesis and physical deformities. Although more than 50 clinical manifestations have been described, only two major criteria or one major and two minor criteria are necessary for diagnosis. The most frequently observed manifestation in the oral and the maxillofacial region is an odontogenic keratocyst. In this study, we describe a 14‐year‐old boy with a diagnosis of NBCCS who presented with a central odontogenic fibroma (COF) in the mandible. This report highlights the importance of precise diagnosis and the choice of surgical method for COF.