Open AccessA rare, highly aggressive primitive neuroectodermal tumor of the kidney: Case report and literature review
Author(s) -
Chin-Chuan Su,
ChienLiang Liu,
Ching-Nan Lin,
Ying-Huei Lee,
KunHung Shen
Publication year - 2012
Publication title -
urological science
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.155
H-Index - 8
eISSN - 1879-5234
pISSN - 1879-5226
DOI - 10.1016/j.urols.2012.03.001
Subject(s) - medicine , computed tomographic , primitive neuroectodermal tumor , abdomen , lung , metastasis , kidney , immunohistochemistry , abdominal pain , weight loss , chemotherapy , radiology , surgery , pathology , computed tomography , cancer , obesity
We report a case of a 14-year-old boy who initially suffered from a sudden onset of abdominal pain for 2 weeks with a protrusive soft mass over the left upper abdomen. No obvious symptomatic symptoms or body weight loss were observed. However, early lung metastasis was detected after an initial computed tomographic examination. Even after we performed salvage en bloc resection of the huge retroperitoneal tumor after primary neoadjuvant chemotherapy, the final outcome was still poor. A diagnosis according to radiologic findings was uncharacteristic. Finally, a pathologic diagnosis based on histologic and immunohistochemical results revealed a rare renal peripheral primitive neuroectodermal tumor