CMR-Based Characterization of Cardiac Amyloidosis
Author(s) -
Andrea Barison,
Pier Giorgio Masci,
Giovanni Donato Aquaro
Publication year - 2014
Publication title -
jacc. cardiovascular imaging
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 5.79
H-Index - 120
eISSN - 1936-878X
pISSN - 1876-7591
DOI - 10.1016/j.jcmg.2014.04.020
Subject(s) - transthyretin , amyloidosis , cardiac amyloidosis , restrictive cardiomyopathy , cardiomyopathy , medicine , amyloid fibril , cardiology , al amyloidosis , immunoglobulin light chain , disease , pathology , heart failure , immunology , antibody , amyloid β
Amyloidosis is a systemic disease caused by the deposition of misfolded proteins. Cardiac involvement is a major cause of morbidity and mortality, especially in the light chain (AL) and transthyretin (ATTR) forms. Amyloidosis usually presents as a restrictive cardiomyopathy with progressive systolic
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