Open AccessMonolobar Caroli’s disease with renal cysts: Case report
Author(s) -
Shruti Thakur,
Sushma Makhaik,
Anubhav Chauhan,
Anupam Jhobta,
Charu Smita Thakur,
Rajeev Sood
Publication year - 2014
Publication title -
the egyptian journal of radiology and nuclear medicine /the egyptian journal of radiology and nuclear medicine
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.19
H-Index - 13
eISSN - 2090-4762
pISSN - 0378-603X
DOI - 10.1016/j.ejrnm.2013.10.007
Subject(s) - congenital hepatic fibrosis , medicine , intrahepatic bile ducts , cirrhosis , disease , etiology , biliary cirrhosis , gastroenterology , pathology , hepatic fibrosis , fibrosis , bile duct , portal hypertension , autoimmune disease
Caroli’s disease is autosomal recessive, non-obstructive dilatation of intrahepatic biliary ducts. The exact etiology is unclear. Two variants of Caroli’s disease are well known-simple; in which bile ducts are dilated without hepatic fibrosis and the second type which is associated with congenital hepatic fibrosis along with its sequelae, also known as Caroli’s syndrome. Simple Caroli’s disease without hepatic fibrosis is quite rare. The importance of recognizing this disease as a cause of biliary stasis is its frequent association with lithiasis, recurrent cholangitis, liver abscesses, cirrhosis and cholangiocarcinoma