Open AccessHirayama disease in unilateral and bilateral forms-3 case reports
Author(s) -
Shruti Thakur,
Rajeev Sood,
Anupam Jhobta,
Dinesh Dutt Sharma,
Sushma Makhaik,
Neeti Aggarwal,
Charu Smita Thakur
Publication year - 2013
Publication title -
the egyptian journal of radiology and nuclear medicine /the egyptian journal of radiology and nuclear medicine
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.19
H-Index - 13
eISSN - 2090-4762
pISSN - 0378-603X
DOI - 10.1016/j.ejrnm.2013.01.004
Subject(s) - medicine , weakness , atrophy , surgery , disease , spinal cord , spinal cord compression , radiology , physical medicine and rehabilitation , pathology , psychiatry
Hirayama disease is a benign, nonprogressive motor neuron disease affecting the upper limbs. It is secondary to an abnormal anterior displacement of the posterior dura with secondary compression of the lower cervical spinal cord. It should be suspected in young male patients with a chronic history of weakness and atrophy involving the upper extremities followed by clinical stability in few years. The involvement is usually unilateral but may be bilateral. MR imaging is the best way to make the diagnosis but it necessitates the use of both extension/flexion and post contrast studies