Open AccessGlomangiopericytoma: An uncommon sinonasal perivascular tumor with particular characteristics
Author(s) -
Mehdi Chihani,
Abdelfattah Aljalil,
Mohamed Touati,
Y. Zoubeir,
A. Labraïmi,
Haddou Ammar,
Brahim Bouaity
Publication year - 2011
Publication title -
egyptian journal of ear nose throat and allied sciences
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.108
H-Index - 8
eISSN - 2090-3405
pISSN - 2090-0740
DOI - 10.1016/j.ejenta.2012.01.001
Subject(s) - pathology , medicine
Glomangiopericytoma, sinonasal type hemangiopericytoma, is a rare sinonasal neoplasm with a perivascular myoid phenotype, and accounts for less than 0.5% of all sinonasal tumors. It is considered a distinct entity and differs from conventional soft-tissue hemangiopericytoma in location, clinical and histopathologic features. Glomangiopericytoma is a borderline low malignancy tumor with a good prognosis after complete surgical resection. We present the case of a 19-year-old girl presented with a progressive nasal obstruction, anosmia and epistaxis. Rhinoscopic examination and imaging studies showed a mass occupying the left nasal cavity without bone destruction. The tumor was removed successfully by endoscopic endonasal surgery. The anatomopathology examination with immunohistochemistry confirmed the diagnosis of glomangiopericytoma. In the light of this observation and a literature review, clinical aspects, histological characteristics, therapeutic principles and prognosis of this tumor will be discussed