Open AccessMembranous septal aneurysm in a child with Noonan syndrome and hypertrophic cardiomyopathy
Author(s) -
Priyadarshini Arunakumar,
Usha M.K. Sastry,
Ramya Guddekeri Satyamurthy,
Jayaranganath Mahimarangaiah
Publication year - 2022
Publication title -
indian journal of thoracic and cardiovascular surgery/indian journal of thoracic and cardiovascular surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.114
H-Index - 9
eISSN - 0973-7723
pISSN - 0970-9134
DOI - 10.1007/s12055-021-01287-x
Subject(s) - medicine , interventricular septum , hypertrophic cardiomyopathy , ventricular outflow tract obstruction , cardiology , noonan syndrome , aneurysm , ventricular outflow tract , septal myectomy , cardiac surgery , heart septum , anatomy , surgery , obstructive cardiomyopathy , ventricle
A 4-year-old boy was diagnosed with hypertrophic cardiomyopathy with moderate degree of obstruction of the left ventricular outflow tract, secondary to asymmetric septal hypertrophy during infancy. Echocardiogram on follow-up showed increase in left ventricular outflow tract obstruction and appearance of an aneurysm in the membranous portion of interventricular septum. The appearance of the membranous septal aneurysm may be related to the direction of jet arising from the point of contact of the anterior mitral leaflet with the hypertrophied basal septum and hitting this part of the interventricular septum.