
Berry syndrome—a rare congenital cardiac anomaly
Author(s) -
Maruti Haranal,
Balaji Srimurugan,
Duyen Mai Dinh,
Sivakumar Sivalingam
Publication year - 2021
Publication title -
indian journal of thoracic and cardiovascular surgery/indian journal of thoracic and cardiovascular surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.114
H-Index - 9
eISSN - 0973-7723
pISSN - 0970-9134
DOI - 10.1007/s12055-021-01206-0
Subject(s) - cardiac surgery , medicine , cardiothoracic surgery , hypoplasia , cardiology , interrupted aortic arch , ductus arteriosus , vascular surgery , aortic arch , pulmonary artery , surgery , aorta
Berry syndrome is a rare congenital cardiac anomaly, characterized by distal aortopulmonary window, hypoplasia or interruption of the aortic arch, intact ventricular septum, and aortic origin of the right pulmonary artery and patent ductus arteriosus. Anatomic depiction of each component is important for the diagnosis. Single-stage surgical repair is challenging but feasible with good survival outcomes. The available literature on this anomaly is limited. Hence, this paper aims at reviewing the literature on Berry syndrome.