Open AccessHypoplastic left heart syndrome: current modalities of treatment and outcomes
Author(s) -
Smruti R. Mohanty,
Agastya Patel,
Simran Kundan,
Hari Bipin Radhakrishnan,
Sumathi Rao
Publication year - 2020
Publication title -
indian journal of thoracic and cardiovascular surgery/indian journal of thoracic and cardiovascular surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.114
H-Index - 9
eISSN - 0973-7723
pISSN - 0970-9134
DOI - 10.1007/s12055-019-00919-7
Subject(s) - hypoplastic left heart syndrome , cardiac surgery , medicine , vascular surgery , cardiothoracic surgery , intensive care medicine , modalities , surgery , cohort , pediatrics , cardiology , heart disease , social science , sociology
Hypoplastic left heart syndrome is a constellation of malformations which result from the severe underdevelopment of any left-sided cardiac structures. Once considered to be universally fatal, the prognosis for this condition has tremendously improved over the past four decades since the work of William Norwood in the early 1980s. Today, a staged surgical approach is applied for palliating this distinctive cohort of patients, in which they undergo three operative procedures in the first 10 years of their life. Advancements in medical technologies, surgical techniques, and our growing experience in the management of HLHS have made survival into adulthood a possibility. Through this review, we present the different phases of the staged approach with primary focus on stage 1-its modifications, current technique, alternatives, and latest outcomes.