Open AccessAudit of Gastrointestinal Manifestations in Patients with Loeys–Dietz Syndrome and Vascular Ehlers–Danlos Syndrome
Author(s) -
Xiao Jing Wang,
Mary Babameto,
Dusica BabovicVuksanovic,
Juan M. Bowen,
Michael Camilleri
Publication year - 2020
Publication title -
digestive diseases and sciences
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.14
H-Index - 124
eISSN - 1573-2568
pISSN - 0163-2116
DOI - 10.1007/s10620-020-06265-8
Subject(s) - medicine , ehlers–danlos syndrome , cohort , irritable bowel syndrome , depression (economics) , connective tissue disorder , surgery , general surgery , economics , macroeconomics
Loeys-Dietz syndrome (LDS) and vascular Ehlers-Danlos Syndrome (vEDS) are genetically heterogeneous heritable disorders of connective tissue. Both are multi-system disorders with dominant vascular pathology and associated gastrointestinal manifestations.