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An unusual case of duodenal obstruction‐gangliocytic paraganglioma
Author(s) -
Mann C. M.,
Bramhall S. R.,
Buckels J. A.,
Taniere P.
Publication year - 2009
Publication title -
journal of hepato‐biliary‐pancreatic surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.63
H-Index - 60
eISSN - 1868-6982
pISSN - 0944-1166
DOI - 10.1007/s00534-009-0092-8
Subject(s) - medicine , pancreaticoduodenectomy , paraganglioma , lymph node , diverticulum (mollusc) , abdominal pain , presentation (obstetrics) , gastrointestinal tract , general surgery , radiology , pancreas , surgery , pathology
Gangliocytic paragangliomas are rare tumors located in the gastrointestinal tract that are considered to be benign. They are composed of spindle‐shaped cells, epithelioid cells, and ganglion‐like cells. They usually present with abdominal pain, and/or gastrointestinal bleeding, and occasionally with obstructive jaundice. We report a case of obstruction in a 17‐year‐old female, which on histology was found to be a gangliocytic paraganglioma, with an extremely unusual presentation. Intraoperatively, the patient was found to have local tumor extension and regional lymph node invasion, and so she underwent a pylorus‐preserving pancreaticoduodenectomy, with local lymph node clearance. We discuss the management of this unusual case and review the literature.