Open AccessDevelopmentally anomalous cerebellar encephalocele arising within the cerebellopontine angle and extending into the adjacent skull base in a pediatric patient
Author(s) -
Forrest Hamrick,
Michael Karsy,
Carol S. Bruggers,
Angelica R. Putnam,
Gary L. Hedlund,
Samuel Cheshier
Publication year - 2021
Publication title -
child's nervous system
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.46
H-Index - 84
eISSN - 1433-0350
pISSN - 0256-7040
DOI - 10.1007/s00381-020-05020-8
Subject(s) - cerebellopontine angle , medicine , anatomy , encephalocele , palsy , skull , cerebellar ataxia , magnetic resonance imaging , temporal bone , presentation (obstetrics) , neurosurgery , ataxia , radiology , pathology , alternative medicine , psychiatry
Lesions of the cerebellopontine angle (CPA) in young children are rare, with the most common being arachnoid cysts and epidermoid inclusion cysts. The authors report a case of an encephalocele containing heterotopic cerebellar tissue arising from the right middle cerebellar peduncle and filling the right internal acoustic canal in a 2-year-old female patient. Her initial presentation included a focal left 6th nerve palsy. Magnetic resonance imaging was suggestive of a high-grade tumor of the right CPA. The lesion was removed via a retrosigmoid approach, and histopathologic analysis revealed heterotopic atrophic cerebellar tissue. This report is the first description of a heterotopic cerebellar encephalocele within the CPA and temporal skull base of a pediatric patient.