Open AccessAlveolar rhabdomyosarcoma of paranasal sinus with cervical metastasis-a case report
Author(s) -
Dipak Ranjan Nayak,
R. Balakrishnan,
A. S. Shahab,
Laxmi Rao
Publication year - 2000
Publication title -
indian journal of otolaryngology and head and neck surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.229
H-Index - 22
eISSN - 2231-3796
pISSN - 0973-7707
DOI - 10.1007/bf03000338
Subject(s) - medicine , rhabdomyosarcoma , paranasal sinuses , sinus (botany) , otorhinolaryngology , radiation therapy , alveolar rhabdomyosarcoma , head and neck , surgery , incidence (geometry) , lymph node metastasis , chemotherapy , radical surgery , radiology , metastasis , sarcoma , pathology , cancer , botany , physics , optics , biology , genus
Rhabdomyosarcoma (RMS) is a rare tumour in adults and involvement of paranasal sinuses is extremely rare comprising only 1.5% of reported head and neck rhabdomyosarcomas. Alveolar type, a rarer form of RMS, mainly seen in adults, has the worst prognosis. Incidence of lymph node metastases is more common in this type, compared to the other forms. An aggressive combined modality of treatment has dramatically improved the poor survival statistics noted previously. Our experience with one such case occurring in paranasal sinus and orbit which was managed by surgery multidrug chemotherapy & radical radiotherapy is discussed and relevant literature has been reviewed.