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Lipids of liver, kidney, spleen and muscle in a case of generalized deficiency of cytochrome b 5 reductase in congenital methemoglobinemia with mental retardation
Author(s) -
Hirono Haruko
Publication year - 1984
Publication title -
lipids
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.601
H-Index - 120
eISSN - 1558-9307
pISSN - 0024-4201
DOI - 10.1007/bf02534610
Subject(s) - kidney , medicine , clinical chemistry , endocrinology , spleen , reductase , lipidology , linoleic acid , cytochrome , biology , chemistry , biochemistry , fatty acid , enzyme
The lipid compositions of liver, kidney, spleen and muscle in a case of generalized deficiency of cytochrome b 5 reductase in congenital methemoglobinemia with mental retardation were analyzed and compared with age‐matched controls. The contents of cholesterol and phospholipids (μmol/g) in each organ were within the normal range. Diminished proportions of unsaturated fatty acids were observed in ethanolamine phosphoglycerides (EPG) of the liver. The proportion of linoleic acid decreased to less than half of the normal level in EPG of liver, kidney and spleen.