z-logo
Premium
Haemodialysis for metabolic decompensation in propionic acidaemia
Author(s) -
Roth B.,
YounossiHartenstein A.,
Skopnik H.,
Leonard J. V.,
Lehnert W.
Publication year - 1987
Publication title -
journal of inherited metabolic disease
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.462
H-Index - 102
eISSN - 1573-2665
pISSN - 0141-8955
DOI - 10.1007/bf01800040
Subject(s) - metabolic acidosis , medicine , decompensation , acidosis , cardiac decompensation , respiratory acidosis , intensive care medicine , pediatrics , propionic acidemia , metabolic disease , anesthesia , heart failure
During an acute respiratory infection, a 4‐year‐old girl with propionic acidaemia deteriorated rapidly, becoming comatose with a marked acidosis. She did not respond to standard treatment but during haemodialysis her clinical state quickly improved.

This content is not available in your region!

Continue researching here.

Having issues? You can contact us here