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Nutritional value of essential amino acids in the treatment of adults with phenylketonuria
Author(s) -
Dotremont H.,
François B.,
Diels M.,
Gillis P.
Publication year - 1995
Publication title -
journal of inherited metabolic disease
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.462
H-Index - 102
eISSN - 1573-2665
pISSN - 0141-8955
DOI - 10.1007/bf00711746
Subject(s) - lysine , nitrogen balance , limiting , medicine , amino acid , endocrinology , chemistry , biochemistry , nitrogen , mechanical engineering , organic chemistry , engineering
Conclusion The present short‐term N‐balance study in adult PKU patients receiving a mixture of LNAA establishes a limited retention of nitrogen. Whether lysine could be the limiting amino acid remains to be determined by new short‐term N‐balance studies, with lysine added to the LNAA mixture. Therefore, special caution should be taken in the long‐term use in PKU patients of LNAA without any added lysine.