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A case of restrictive cardiomyopathy presenting in fetal life with an isolated pericardial effusion
Author(s) -
Sekar P.,
Hornberger L. K.,
Smallhorn J. S.
Publication year - 2010
Publication title -
ultrasound in obstetrics and gynecology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 3.202
H-Index - 141
eISSN - 1469-0705
pISSN - 0960-7692
DOI - 10.1002/uog.7510
Subject(s) - medicine , pericardial effusion , restrictive cardiomyopathy , cardiomyopathy , pregnancy , cardiology , gestation , fetus , hydrops fetalis , heart disease , pericardium , cardiac function curve , surgery , heart failure , biology , genetics
We describe the evolution during pregnancy of a case of restrictive cardiomyopathy which first presented at 22 weeks' gestation with a large pericardial effusion. Measurements of cardiac function were normal and remained near normal until late in the third trimester, when pulsed and tissue Doppler data suggested impairment in ventricular relaxation. This disease progressed in postnatal life to symptomatic restrictive cardiomyopathy by 2 years of age necessitating cardiac transplant. To our knowledge, this is the first time this unusual association has been reported. Copyright © 2010 ISUOG. Published by John Wiley & Sons, Ltd.