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EP15.07: Megalourethra: a case report with poor neonatal outcome
Author(s) -
Lange S.,
Pellegrinelli J.
Publication year - 2019
Publication title -
ultrasound in obstetrics and gynecology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 3.202
H-Index - 141
eISSN - 1469-0705
pISSN - 0960-7692
DOI - 10.1002/uog.21388
Subject(s) - medicine , pulmonary hypoplasia , urethra , oligohydramnios , hypoplasia , hydronephrosis , urinary tract obstruction , surgery , corpus spongiosum , cystoscopy , glans penis , urinary system , penis , pregnancy , gestation , genetics , biology
Megalourethra is a rare cause of low urinary tract obstruction (LUTO), with a typical presentation of megacystis and an additional image of dilated penile urethra. It results from absence or hypoplasia of the corpus spongiosum or corpus cavernosum, or it is caused by anterior urethral valves. It can be associated with anal, limb or cardiac anomalies. Spontaneous resolution is less than LUTO due to other causes, same as survival rate and normal renal function at long-term. The overall prognosis depends on the associated anomalies and renal impairment. As other types of LUTO, mortality is due to pulmonary hypoplasia associated with oligohydramnios, and morbidity to chronic progressive renal failure and end-stage renal disease (ESRD).