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Individualized robotic organ‐sparing surgery in a paediatric case of renal perivascular epithelioid cell tumour
Author(s) -
Silveri Massimiliano,
Natali Gian Luigi,
Cobellis Giovanni,
Roberti Agnese,
Rossi Sabrina,
Gregori Lorenzo,
Torino Giovanni
Publication year - 2020
Publication title -
the international journal of medical robotics and computer assisted surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.556
H-Index - 53
eISSN - 1478-596X
pISSN - 1478-5951
DOI - 10.1002/rcs.2142
Subject(s) - medicine , biopsy , kidney , perivascular epithelioid cell , radiology , robotic surgery , clear cell , epithelioid cell , surgery , pathology , renal cell carcinoma , immunohistochemistry
Background Perivascular epithelioid cell tumours (PEComas) represent a rare group of mesenchymal tumours with an unpredictable outcome. They are usually observed in middle‐aged women whilst they are very rare in children, with limited cases described. Due to the rare anatomical location in kidneys, a correct diagnosis and treatment is really challenging. Methods We observed and treated a case of kidney's PEComa in a 14‐year‐old boy. Results An individualized approach based on anatomical (3D CT‐reconstructions) and histopathological (US‐guided preliminary biopsy) features lead us to perform a successful robotic‐sparing surgery enabling the preservation of two‐thirds of the kidney involved. Conclusions A meticulous preoperative planning in selected patients can lead to a minimally invasive approach even in some paediatric kidney's neoplasms.