Open AccessSjögren's syndrome with nodular pulmonary amyloidosis
Author(s) -
Wu ChangWei,
Chien YingChun
Publication year - 2021
Publication title -
respirology case reports
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.304
H-Index - 9
ISSN - 2051-3380
DOI - 10.1002/rcr2.699
Subject(s) - medicine , amyloidosis , pathology , rheumatoid arthritis , al amyloidosis , lymphoma , malt lymphoma , amyloid (mycology) , immunology , immunoglobulin light chain , antibody
We report a case of Sjögren's syndrome with nodular pulmonary amyloidosis. Amyloidosis is a heterogeneous group of diseases caused by aggregation of autologous protein and its extracellular deposition as fibrils. Most cases of nodular pulmonary amyloidosis are the result of an underlying disorder such as mucosa‐associated lymphoid tissue lymphoma, rheumatoid arthritis, or multiple myeloma. Nodular pulmonary amyloidosis with Sjögren's syndrome is very rare. The clinical outcome of patients with nodular pulmonary amyloidosis is good if the underlying disease can be controlled.