Open AccessBronchial varices in a child with tricuspid atresia six years post Fontan correction
Author(s) -
Bhushan Shreya,
Goyal Vikas,
Ward Cameron,
Rashid Muddassir,
Kapur Nitin
Publication year - 2020
Publication title -
respirology case reports
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.304
H-Index - 9
ISSN - 2051-3380
DOI - 10.1002/rcr2.620
Subject(s) - medicine , tricuspid atresia , varices , embolization , radiology , atresia , bronchial artery , cardiac catheterization , angiography , fontan procedure , regurgitation (circulation) , cardiology , surgery , heart disease , cirrhosis
Tracheal and bronchial varices are rarely found in children. However, they have been described in adults with failing Fontan circuits or secondary to vascular pathology, such as portal and pulmonary hypertension. We report the presentation of haemoptysis and bronchial varices in a child, six years after a Fontan procedure for tricuspid atresia. She had tortuous mediastinal and transpleural arterial collaterals on computed tomography (CT) angiography and cardiac catheterization and subsequently underwent embolization of these collaterals. While the haemoptysis settled post embolization, the bronchial varices persisted on repeat bronchoscopy. She has since been clinically well with no further haemoptysis.