Open AccessGiant intrapulmonary malignant peripheral nerve sheath tumour
Author(s) -
Desdiani Desdiani,
Darifah Siti,
Azali Chairul
Publication year - 2020
Publication title -
respirology case reports
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.304
H-Index - 9
ISSN - 2051-3380
DOI - 10.1002/rcr2.567
Subject(s) - medicine , malignant peripheral nerve sheath tumor , soft tissue , thoracotomy , pathology , biopsy , lung , immunohistochemistry , nerve sheath neoplasm , nerve sheath , peripheral , surgery , schwannoma
Pulmonary malignant peripheral nerve sheath tumours (MPNSTs) are extremely rare soft tissue sarcomas that develop from the cell constituting the nerve sheaths, approximately 5–10% of all soft tissue sarcomas. We present a rare case of primary lung MPNST in an adult female non‐smoker patient, in whom surgical thoracotomy approach has obtained a good control of the disease. Low‐grade MPNST was established from excisional biopsy followed by immunohistochemistry.