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Pulmonary growth abnormalities as etiologies for pediatric pulmonary hypertension
Author(s) -
Mallory George B.,
Spielberg David R.,
SilvaCarmona Manuel
Publication year - 2021
Publication title -
pediatric pulmonology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.866
H-Index - 106
eISSN - 1099-0496
pISSN - 8755-6863
DOI - 10.1002/ppul.24998
Subject(s) - medicine , pulmonary hypertension , etiology , abnormality , disease , lung , interstitial lung disease , broad spectrum , radiography , lung disease , respiratory disease , pulmonary disease , pathology , radiology , intensive care medicine , chemistry , psychiatry , combinatorial chemistry
Pulmonary growth abnormality (PGA) is a common type of diffuse lung disease in infants. Although the histologic and radiographic features of PGA have been described in the literature in varying detail, the clinical spectrum of disease has not. The array of case series and case reports has led to a clinical picture that could be confusing to clinicians. We describe three subsets of PGA, including its association with the histologic marker of pulmonary interstitial glycogenosis, and its common association with pulmonary hypertension. We propose a new approach to what we consider an increasingly broad array of different disease entities.