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Enhancing care for individuals with advanced cystic fibrosis lung disease
Author(s) -
Kapnadak Siddhartha G.,
Ramos Kathleen J.,
Dellon Elisabeth P.
Publication year - 2021
Publication title -
pediatric pulmonology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.866
H-Index - 106
eISSN - 1099-0496
pISSN - 8755-6863
DOI - 10.1002/ppul.24937
Subject(s) - medicine , cystic fibrosis , psychosocial , lung transplantation , intensive care medicine , referral , lung disease , quality of life (healthcare) , lung , disease , palliative care , medical care , family medicine , nursing , psychiatry
While remarkable advances in cystic fibrosis (CF) care have led to improvements in survival and quality of life, many individuals with CF are living with advanced cystic fibrosis lung disease (ACFLD) and others will face continued disease progression and its associated complex treatments and choices. This review will provide a summary of recently published guidelines for ACFLD care and lung transplant referral and highlight ongoing work to enhance the care of those with ACFLD through improvements in medical and psychosocial care, palliative care, and care around lung transplantation.