Premium
Clinical approach to cardiac pauses in congenital central hypoventilation syndrome
Author(s) -
Mitacchione Gianfranco,
Bontempi Luca,
Curnis Antonio
Publication year - 2019
Publication title -
pediatric pulmonology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.866
H-Index - 106
eISSN - 1099-0496
pISSN - 8755-6863
DOI - 10.1002/ppul.24189
Subject(s) - medicine , asystole , congenital central hypoventilation syndrome , hypoventilation , bradycardia , sinus bradycardia , cardiac pacing , cardiology , rhythm , autonomic nervous system , anesthesia , heart rate , respiratory system , blood pressure
Congenital central hypoventilation syndrome (CCHS) patients may have heart rhythm disorders related to autonomic nervous system dysfunction such as, sinus bradycardia and transient asystole with potentially dramatic syncopal events. The diagnosis of these cardiac alterations may be challenging with conventional periodical Holter monitoring. The case shows how continuous heart rhythm monitoring provided by the implantable cardiac monitor (ICM) may play a crucial role for their early diagnosis and the choice of the appropriate therapeutic intervention.