Survival of a child with spinal muscular atrophy and acute respiratory distress syndrome | Zendy

Wampole Anthony | Zendy; Schroth Mary | Zendy; Boriosi Juan | Zendy

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Survival of a child with spinal muscular atrophy and acute respiratory distress syndrome

Author(s) -

Wampole Anthony,

Schroth Mary,

Boriosi Juan

Publication year - 2015

Publication title -

pediatric pulmonology

Language(s) - English

Resource type - Journals

SCImago Journal Rank - 0.866

H-Index - 106

eISSN - 1099-0496

pISSN - 8755-6863

DOI - 10.1002/ppul.23171

Subject(s) - medicine , spinal muscular atrophy , mechanical ventilation , ards , respiratory distress , sma* , intensive care unit , pediatric intensive care unit , sedation , ventilation (architecture) , anesthesia , intensive care medicine , pediatrics , lung , disease , mechanical engineering , mathematics , combinatorics , engineering

Summary Spinal muscular atrophy (SMA), a lower motor neuron anterior horn cell disease, causes significant respiratory morbidity and mortality in children. Acute respiratory distress syndrome (ARDS) accounts for 1–4% of all Pediatric Intensive Care Unit (PICU) admissions. Management outcomes for ARDS in patients with SMA have not been described. We present the case of a 5‐year‐old boy with Type II SMA and ARDS requiring invasive mechanical ventilation. He improved with meticulous management of mechanical ventilation, airway clearance, fluid/nutrition, and sedation/analgesia. He was successfully extubated after 14 days of invasive mechanical ventilation and discharged home after a 20 day hospitalization. Pediatr Pulmonol. 2015; 50:E29–E31. © 2015 Wiley Periodicals, Inc.

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