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An atypical presentation of pulmonary air‐leak syndrome and multisystem toxic epidermal necrolysis
Author(s) -
Ellenburg Joseph T.,
Josey David
Publication year - 2014
Publication title -
pediatric pulmonology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.866
H-Index - 106
eISSN - 1099-0496
pISSN - 8755-6863
DOI - 10.1002/ppul.22908
Subject(s) - medicine , toxic epidermal necrolysis , presentation (obstetrics) , dermatology , intensive care medicine , surgery
Summary Toxic epidermal necrolysis (TEN) is a rare and potentially fatal mucocutaneous condition that may affect both children and adults. TEN mortality rates vary greatly between both patient populations, but multisystem involvement is common. Management presents many challenges as there is no specific therapy for TEN, and patients often require the expertise of burn units. We report a child who survived TEN with multisystem involvement including the rare but life threatening occurrence of a pulmonary air‐leak syndrome while also reviewing controversies surrounding TEN's pathophysiology, sequelae, and multidisciplinary approach to management. Pediatr Pulmonol. 2014; 49:E130–E134. © 2014 Wiley Periodicals, Inc.