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Festival food coma in cystic fibrosis
Author(s) -
Pandit Chetan,
Graham Christie,
Selvadurai Hiran,
Gaskin Kevin,
Cooper Peter,
van Asperen Peter
Publication year - 2013
Publication title -
pediatric pulmonology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.866
H-Index - 106
eISSN - 1099-0496
pISSN - 8755-6863
DOI - 10.1002/ppul.22702
Subject(s) - medicine , decompensation , cystic fibrosis , cirrhosis , portal hypertension , hepatic encephalopathy , liver disease , encephalopathy , gastroenterology , liver function , coma (optics) , disease , intensive care medicine , physics , optics
Abstract Children with cystic fibrosis liver disease and portal hypertension are at risk of developing acute hepatic encephalopathy. Even in the presence of normal synthetic liver function these children may have porto‐systemic shunting. We report a case of an adolosecent who had cystic fibrosis liver disease and presented with life threatening hepatinc encephalopathy. This case illustrates that it is necessary to consider an appropriate dietary regimen in adolosecents with liver disease to prevent hepatic decompensation. Pediatr Pulmonol. 2013; 48:725–727. © 2012 Wiley Periodicals, Inc.