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Lung function in hyper IgE syndrome
Author(s) -
Roxo P.,
Torres L.A.G.M.,
Menezes U.P.,
Melo J.M.L.
Publication year - 2013
Publication title -
pediatric pulmonology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.866
H-Index - 106
eISSN - 1099-0496
pISSN - 8755-6863
DOI - 10.1002/ppul.22532
Subject(s) - bronchiectasis , medicine , allergic bronchopulmonary aspergillosis , pulmonary function testing , lung , atelectasis , respiratory system , immunoglobulin e , respiratory disease , intensive care medicine , immunology , antibody
Pneumatoceles and bronchiectasis are secondary complications of respiratory infections in patients with hyper IgE syndrome (HIgES). We report on a patient with HIgES and recurrent pneumonias since 1 year of age, with progression to pneumatoceles and bronchiectasis and fatal outcome, with disseminated infection and suspected allergic bronchopulmonary aspergillosis, who was subjected to sequential spirometric assessment. We describe the early beginning of respiratory infections, difficulties in the management of pulmonary sequelae and the impact of an early functional diagnosis and follow‐up of the patient regarding a disease for which lung function has not been fully described. Pediatr Pulmonol. 2013; 48:81–84. © 2012 Wiley Periodicals, Inc.