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Cyanosis when head turned to left in an infant with primary ciliary dyskinesia
Author(s) -
Vermeulen Bas,
Haarman Eric,
Rammeloo Lukas,
Hruda Jaroslav
Publication year - 2013
Publication title -
pediatric pulmonology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.866
H-Index - 106
eISSN - 1099-0496
pISSN - 8755-6863
DOI - 10.1002/ppul.22529
Subject(s) - dextrocardia , medicine , primary ciliary dyskinesia , situs inversus , dyskinesia , right atrium , persistent left superior vena cava , left atrium , pulmonary vein , superior vena cava , surgery , cardiology , anatomy , atrial fibrillation , bronchiectasis , lung , coronary sinus , disease , parkinson's disease
A 19‐month‐old boy with primary ciliary dyskinesia (PCD), mirror‐image dextrocardia, situs inversus (SI) totalis suffered from persistent hypoxia. Cyanosis became clinically evident when the child turned the head to the left and resolved after turning the head to the right. Echocardiography demonstrated two superior caval veins; the left sided superior vena cava (SVC) entering the left sided right atrium (RA) and the right sided into the right sided left atrium (LA). Surgical redirection of the right sided caval vein into RA was performed. Pediatr Pulmonol. 2013; 48:88–90. © 2012 Wiley Periodicals, Inc.