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Inspiratory muscle training in Morquio's syndrome: A case study
Author(s) -
Savci Sema,
Ozturk Melda,
InalInce Deniz,
Gultekin Zuhal,
Arikan Hulya,
Sivri H. Serap Kalkanoglu
Publication year - 2006
Publication title -
pediatric pulmonology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.866
H-Index - 106
eISSN - 1099-0496
pISSN - 8755-6863
DOI - 10.1002/ppul.20500
Subject(s) - medicine , aerobic exercise , exertion , physical therapy , muscle strength , quality of life (healthcare) , strength training , muscle weakness , pulmonary function testing , weakness , respiratory system , physical medicine and rehabilitation , cardiology , surgery , nursing
We reported a case of MPS IV A presented with dyspnea on exertion and respiratory muscle weakness. The patient underwent inspiratory muscle training (IMT) using threshold loading for 18 weeks. After 6 weeks of initial IMT, aerobic exercise training consisting of walking was added to the treatment program. Inspiratory muscle strength increased 70%, and 6‐minute walk test (6MWT) distance increased to 47 m. With the inclusion of aerobic exercise training, additional increases in inspiratory muscle strength (7%) and 6MWT distance (26.5 m) were obtained. Exertional dyspnea improved from severe to slight after 6 weeks of IMT, and to very slight after additional 12 weeks of combined aerobic training and IMT. Health‐related quality of life improved especially in social function, emotional function, vitality, and physical role. In conclusion, inspiratory muscles can be trained with the improvement of muscle strength in a patient with Morquio's syndrome. Pediatr Pulmonol. 2006; 41:1250–1253. © 2006 Wiley‐Liss, Inc.