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Pulmonary Agenesis Associated with Dextrocardia, Sternal Defects, and Ectopic Kidney
Author(s) -
Eroglu Atilla,
Alper Fatih,
Turkyilmaz Atila,
Karaoglanoglu Nurettin,
Okur Adnan
Publication year - 2005
Publication title -
pediatric pulmonology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.866
H-Index - 106
eISSN - 1099-0496
pISSN - 8755-6863
DOI - 10.1002/ppul.20301
Subject(s) - dextrocardia , medicine , agenesis , ectopic kidney , radiology , kidney , surgery
Pulmonary agenesis is a rare embryological defect, usually unilateral, and is associated with skeletal, cardiovascular, and other anomalies. A 22‐month‐old girl was admitted to our clinic with recurrent pulmonary infections. A chest X‐ray and multidetector computed tomography (MDCT) revealed pulmonary agenesis with dextrocardia, sternal defects, and a right pelvic ectopic kidney. We report on the first known case of right‐sided pulmonary agenesis combined with isolated dextrocardia, sternal defects, and an ectopic kidney. The importance of MDCT for the diagnosis of pulmonary agenesis and associated other anomalies is demonstrated. Pediatr Pulmonol. © 2005 Wiley‐Liss, Inc.