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Generalized lymphangiomatosis and chylothorax in the pediatric age group
Author(s) -
Shah A. R.,
Dinwiddie R.,
Woolf D.,
Ramani R.,
Higgins J. N. P.,
Matthew D. J.
Publication year - 1992
Publication title -
pediatric pulmonology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.866
H-Index - 106
eISSN - 1099-0496
pISSN - 8755-6863
DOI - 10.1002/ppul.1950140211
Subject(s) - lymphangiomatosis , medicine , chylothorax , histology , presentation (obstetrics) , immunohistochemistry , pathology , lymphatic system , radiology
Four patients with generalized lymphangiomatosis presenting with chylothoraces are described. All four had bone involvement, two had involvement of the spleen, and one of the pericardium. The diagnosis was confirmed by typical radiology, histology, and in three patients by immunohistochemistry. Treatment was mainly palliative. Three patients died within 1/2 to three years of presentation. © 1992 Wiley‐Liss, Inc.