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Tracheomalacia and bronchomalacia associated with larsen syndrome
Author(s) -
Rock Michael J.,
Green Christopher G.,
Pauli Richard M.,
Peters Mary Ellen
Publication year - 1988
Publication title -
pediatric pulmonology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.866
H-Index - 106
eISSN - 1099-0496
pISSN - 8755-6863
DOI - 10.1002/ppul.1950050111
Subject(s) - tracheomalacia , medicine , stridor , tracheobronchomalacia , laryngomalacia , bronchoscopy , airway obstruction , airway , surgery
Bronchomalacia has not previously been described in association with Larsen syndrome. In this article, three children with Larsen syndrome are reported. All three patients have tracheomalacia, and one of them has diffuse bronchomalacia diagnosed at flexible fiberoptic bronchoscopy. The patients' symptoms of airway obstruction include stridor, cyanosis, apnea, and recurrent pneumonias. Recognition of these abnormalities may allow the institution of supportive therapy.