Airway in the oculo‐auriculo‐vertebral spectrum: Two cases and a review of the literature

Two patients with oculo‐auriculo‐vertebral syndrome and multiple airway anomalies are presented. Both patients had esophageal atresia with a distal tracheoesophageal fistula and tracheomalacia due to innominate artery compression. Pulmonary hypoplasia, obstructive sleep apnea, and a laryngeal anomaly were also noted. The literature of airway anomalies and obstructive sleep apnea described in association with the oculo‐auriculo‐vertebral spectrum is reviewed. Pediatr Pulmonol. 2001; 32:250–256. © 2001 Wiley‐Liss, Inc.